박준·양원용·양연모*·이두형·최우석*
경희대학교
의과대학 성형외과학 교실, 한림대학교 의과대학 성형외과학
교실*,
경희대학교 의과대학 진단방사선학교실*
Kasabach-Merritt
syndrome is the association
of thrombocytopenia, disorder of coagulation, spontaneous
bleeding and en1argement of a hemangima or extensive
hemangiomatosis, which can be often life threatening.
We
experienced a three years-old girl with suddenly
enlarging hemangioma of right cheek, complicated
by severe thrombocytopenia, consumptive coagulopathy
and hemorrhagic cystitis. Generalized petechia and
ecchymosis were noted on the overlying skin of hemangioma,
trunk and extremities. By the study of MRI and angiography,
hypervascular mass was located within the right
masseter muscle extending to temporalis muscle and
anterior to parotid gland. So selective
embolization with PVA (polyvinyl alcohol)
was performed through the distal branch of internal
maxillary artery and facial artery. She was medicated
with oral corticosteroid for 3 weeks. After embolization,
blood flow to hemangioma and facial swelling were
markedly decreased.
Patient
was followed up for 7 years and she showed normal
contour of face and no bleeding diathesis.
Key
Words: Kasabach-Merritt syndrome, Selective embo1ization,
Corticosteroid |
