Bum-Jin
Juhn Woo-Young Sim Mu-Hyoung Lee
Annals
of Dermatol 1999;11(3);185-188
Periumbilical
perforating pseudoxanthoma elasticum (PPPXE) is
a localized acquired disorder found most frequently
in obese, multiparous, middle-aged women. It is
characterized clinically by yellowish, lax, well-circumscribed,
reticulated or cobblestoned patches or plaques in
the periumbilical region. Multiparity, obesity,
massive ascites, and abdominal surgery are thought
to the initiating factors. There is controversy
about the etiology of PPPXE. Some authors have classified
it as a separate entity from hereditary pseudoxanthoma
elasticum (PXE), while others speculate that this
condition merely represents a variable expression
of PXE in which systemic associations are likely.We
report a case of periumbilical perforating pseudoxanthoma
elasticum associated with a clinical PXE lesion
on the anterior neck. (Ann Dermatol 11(3) 185~188,1999). |
