H.S.Kim
M.H.Lee W.Y.Sim C.R.Haw Annals of Dermatol
1998;10(1);44-47
Neurofibromatosis
produces a broad spectrum of clinical manifestations.
Cafe-au-lait spots, cutaneous neurofibroma and tumors
of the central and peripheral nervous system are
well known manifestations. One of the more serious
aspects of the disease relates to the arterial involvement.
Renal arterial disease with resultant hypertension
has been paticularly well documented. However, cerebrovascular
lesions in neurofibromatosis are uncommon. Cerebral
arterial occlusive diseases with juxtabasilar telangiectasia
(moyamoya disease) associated with neurofibromatosis
have been documented in about 40 patients in the
world literature. We report a case of neurofibromatosis
associated with the moyamoya disease. (Ann Dermatol
10:(1) 44-47, 1998) |
